Wednesday, October 30, 2013
*PLEASE SEE UPDATED CWD SCIENCE FROM THE PRION2013 CONFERENCE ON POTENTIAL 
CWD TO HUMANS, CATS, MOTHER TO OFFSPRING, GAME FARMS, AND THE ENVIRONMENT, BELOW 
THIS REPORT ABOUT NEW YORK STATE CWD.  ...TSS
Joe Morrissey, 518-457-0752, Joe.Morrissey@agriculture.ny.gov Pete 
Constantakes (DEC), 518-402-8000, pmconsta@gw.dec.state.ny.us 
October 30, 2013 
-------------------------------------------------------------------------------- 
Regulations Issued to Protect NYS Deer Population from Chronic Wasting 
Disease 
Emergency Measures Restrict Importation of Certain Deer Species Disease 
Could Devastate NY’s Deer Population and Result in Severe Economic Repercussions 
on the State’s Sportsman Industry
The New York State Department of Agriculture and Markets and the Department 
of Environmental Conservation today announced emergency regulations to prohibit 
the importation of Chronic Wasting Disease (CWD) susceptible deer into the 
State. The protection of the state’s deer population is important not only to 
the balance of the ecosystem but also is critical to supporting the hundreds of 
thousands of sportsmen and women whose recreational activities contribute some 
$780 million in economic impact statewide.
“These emergency measures will help mitigate the risk of CWD taking a firm 
hold here in New York State,” said State Acting Agriculture Commissioner James 
B. Bays. “I’m a hunter and an avid outdoorsman, and keeping New York’s wild and 
captive deer herds healthy will help protect multi-million dollar industries 
that create jobs and provide recreational opportunities for hundreds of 
thousands of New Yorkers. From our agency’s perspective, the most important 
thing that we can do is limit the exposure of deer to CWD. That’s exactly what 
these regulations will do.”
DEC Commissioner Joe Martens said, "New York State has a long tradition of 
deer hunting and deer management. It is imperative that we remain vigilant and 
prevent Chronic Wasting Disease from entering the State. These regulations will 
bolster existing protections already in place in New York and help to maintain a 
vibrant population of our most sought after game species. This show of 
stewardship help will ensure that sportsmen and sportswomen continue to have 
great deer hunting opportunities throughout the state."
The emergency regulations provide a ban on imports of specific species 
between November 16, 2013 and August 1, 2018. These species include Rocky 
Mountain elk, red deer, mule deer, black-tailed deer, white-tailed deer, sika 
deer, and moose.
Currently 21 states including New York prohibit the importation of certain 
species of live deer. 
CWD is a fatal, neurologic disease to species of deer caused by a disease 
agent called a prion, which eventually destroys the brain tissue of infected 
animals. Prions are shed by infected animals in their saliva, feces and urine. 
The time from infection to the first outward signs of illness (animals appear 
weak and unsteady) may be two years or longer. Soil contaminated with CWD prions 
cannot be decontaminated and can remain as a source of CWD exposure to wild deer 
for years. At the present time, the only accepted means of diagnosis must be 
performed after an animal suspected of being infected with CWD is dead.
The primary tool for preventing spread of CWD is the USDA Herd 
Certification program, which requires herds that wish to ship animals interstate 
to undergo a five year certification process involving surveillance testing and 
maintenance of herd inventories. While the program has helped slow the spread of 
CWD, it cannot guarantee that certified herds will remain CWD-free. Despite the 
best efforts of qualified animal health professionals, CWD has arisen in four 
new states (PA, MO, MN, IA) since 2010 and all were participating in the Herd 
Certification program. The source of the most recent detection of CWD in both 
captive and wild deer in Pennsylvania remains unknown twelve months after the 
initial detection. Farms in other states purchased animals from the original 
infected herd in Pennsylvania; some escaped and some remain unaccounted for. 
Absent these regulations, states with potentially infected deer populations 
would be allowed to export deer to New York.
“If we continue to allow imports, we could receive CWD exposed deer or elk 
that originated in one state and subsequently passed through a facility in a 
third state,” said State Veterinarian, Dr. David Smith. “That’s not a risk we’re 
willing to take here in New York. CWD is extremely difficult to detect and 
control and once present, the costs to the wild deer population, captive deer 
owners, and the entire state are high. We do not want this disease proliferating 
throughout our state’s valuable wild populations and captive deer herds. New 
York will continue to work with stakeholders and animal health professionals as 
these important regulations move forward.”
The costs of states to deal with outbreaks in CWD in terms of resources and 
tax dollars are tremendous. Prevalence rates in some parts of Wisconsin are over 
20 percent just 10 years after the introduction of CWD into the state, costing 
the Wisconsin Department of Natural Resources $14 million the first year alone, 
with much of the money pulled from other wildlife programs.
Furthermore, the economic impact that CWD could have on New York State is 
considerable. Based on the most recent data, New York’s wild deer herds have a 
$780.5 million economic impact in the state, while the economic impact of 
captive deer is $13.2 million. There are an estimated 823,000 hunting licenses 
in New York and the state ranks third in the nation in residential hunters. In 
2011, New York was fourth in the nation in spending by hunters and generated an 
estimated $290 million in state and local taxes.
According to the latest data, there are 433 facilities across New York 
State that currently hold captive deer. Of these facilities, 25 imported a total 
of 400 CWD-susceptible deer from January 1, 2011 through March 29, 2013.
New York will still permit the importation of deer semen for artificial 
insemination. Zoos accredited by the Association of Zoos and Aquariums will also 
be allowed to still import CWD-susceptible species.
Bruce L. Akey, MS DVM, executive director, Animal Health Diagnostic Center, 
College of Veterinary Medicine, Cornell University, said: "The Cornell 
University College of Veterinary Medicine Animal Health Diagnostic Center (AHDC) 
includes internationally recognized experts on the transmission of disease and 
the ecology of diseases in wildlife populations. Chronic Wasting Disease is a 
serious threat to New York's wild white-tailed deer herd. With recent 
confirmation of CWD in Pennsylvania, our disease specialists are very concerned 
that CWD may once again be detected in New York. It is entirely appropriate that 
New York's regulatory agencies, the Department of Agriculture and Markets and 
the Department of Environmental Conservation, take all reasonable measures to 
keep CWD out of New York. Given that there is no test currently available to 
detect CWD in live animals prior to movement, strong prevention measures are the 
only reasonable and economical way of managing CWD. Once CWD is confirmed in a 
population of white-tailed deer, the ecological and economic consequences will 
be catastrophic. We applaud the recent regulation prohibiting the importation of 
live captive white-tailed deer, the highest known risk factor for CWD."
Chuck Parker, president, New York State Conservation Council, said: “The 
New York State Conservation Council takes pride in being a major voice for the 
Sportsmen in New York for over 80 years. All of our positions and policies are 
the majority consensus of our membership. The voting representatives of the 
NYSCC through the affiliations of their local clubs represent upwards of 330,000 
sportsmen in this state. The whitetail deer population in New York is enjoyed by 
sportsmen and outdoor enthusiast alike. The tradition of hunting has a proud 
history in New York and still offers an excellent opportunity for the sportsmen 
today. Along with the opportunity to hunt deer comes the economic impact to the 
state of nearly $800 million from deer hunting. Chronic Wasting Disease, if it 
was to be found in our wild deer population would create a serious 
environmental, recreational, and economic impact in New York. The New York State 
Conservation Council is strongly committed to supporting actions both by the 
Department of Agriculture and Markets and the Department of Environmental 
Conservation to ensure that Chronic Wasting Disease never again is found in New 
York.”
Jason Kemper, chairman of the Conservation Fund Advisory Board, said: “The 
New York State Conservation Fund Advisory Board makes recommendations to state 
agencies on state government plans, policies, and programs affecting fish and 
wildlife. The wild white-tail deer population is extremely valuable to the State 
of New York, generating about $780 million annually by hunting and associated 
businesses. License sales associated with deer hunting fund a majority of the 
Department of Environmental Conservation’s fish and wildlife management 
programs. The health and integrity of New York’s wild deer herd is vital to both 
our natural and hunting heritage as well as our economy. We applaud actions 
taken by the Department of Agriculture and Markets and the Department of 
Environmental Conservation to implement all reasonable measures to prevent CWD 
from ever again occurring in New York.”
Mike Fishman, president of the New York Chapter of The Wildlife Society, 
said: "The New York Chapter of The Wildlife Society strongly supports the joint 
regulatory efforts of the New York State Department of Environmental 
Conservation and the New York State Department of Agriculture and Markets to 
restrict the import of live, captive deer and other cervids to New York to 
prevent the reintroduction of Chronic Wasting Disease (CWD). CWD poses a 
significant threat to our wild deer populations. Reintroduction of the disease 
could have disastrous consequences on an important ecological and economic 
resource in New York. This restriction is a necessary conservation measure to 
protect a very important wildlife resource."
Alan White, executive director of the Catskill Center, said: “The Catskill 
Center supports efforts by both the Department of Agriculture and Markets, and 
the Department of Environmental Conservation to reduce the chances that CWD 
would ever again be found in New York State. We support the newly proposed 
regulation to prohibit the importation of live captive white-tailed deer from 
out of state. These captive deer are a known risk factor for the spread of CWD. 
Deer hunting has deep and rich traditions in the Catskill Mountains, and it is 
vital that we ensure that the health of New York’s wild white-tailed deer herd 
is not compromised by CWD.” A public hearing is scheduled to discuss the 
emergency regulations at noon on December 19, 2013 at the New York State 
Department of Agriculture and Markets, 10B Airline Drive, Albany.
For Release: Tuesday, September 10, 2013
DEC Seeks Hunter Support to Keep Chronic Wasting Disease Out of New 
York
The New York State Department of Environmental Conservation (DEC) reminds 
hunters that Chronic Wasting Disease (CWD) continues to pose a potential threat 
to New York's wild white-tailed deer herd, and hunters should take precautions 
to prevent the spread of the disease. Late last year, CWD was found on a deer 
farm in Pennsylvania and in early 2013, CWD was confirmed in Pennsylvania's wild 
white-tailed deer herd.
"Preventing the introduction of Chronic Wasting Disease into New York is 
vital to protecting our deer herds and is a high priority for DEC," said DEC 
Commissioner Joe Martens. "DEC's deer management and outreach efforts work to 
ensure the health of New York's deer herd and to protect the recreational and 
viewing opportunities deer provide. The most effective way to protect New York's 
deer herd is to keep CWD infectious material out of the state and hunters can 
play an important role in this effort."
CWD is a highly contagious and deadly brain and nervous system disease that 
affects deer, elk, moose and other members of the deer family. CWD is always 
fatal and there are no vaccines or treatment available. The agent that causes 
the disease is called a prion and it is virtually indestructible. Prions are 
found in the lymph nodes, brain and spinal tissues of infected animals, which 
can shed (spread) prions in their urine, saliva, and feces. Also, certain parts 
of dead animals remain infectious on the landscape and in the soil for many 
years. There is no evidence that CWD can infect humans, but DEC urges caution 
when handling or processing CWD susceptible animals.
Individuals who hunt deer, elk or moose outside of New York should be 
familiar with New York's CWD regulation (6 NYCRR Part 189) regarding the 
importation of cervid carcasses and meat back into New York before returning 
home. It is illegal to bring in whole carcasses from any CWD susceptible animal 
taken at a shooting preserve or to bring in whole carcasses from any state or 
province that has had CWD confirmed in wild or captive cervid herds. It is also 
illegal to ship the unprocessed trophy head from those preserves or CWD positive 
states or provinces. It is legal to import finished mounted heads, however. A 
person may only bring back the meat, hide and antlers, and certain parts must be 
removed before entering New York. A full list of prohibited parts can be found 
on DEC's website.
Before leaving to hunt out-of-state:
•Know the CWD status of the state or province you plan to hunt in since it 
can change at any time. For example, four additional states became CWD positive 
in 2012 (Iowa, Michigan, Missouri, and Pennsylvania). •If caught in possession 
of an illegal carcass with the prohibited parts in New York, the carcass will be 
confiscated and destroyed (including antlers, hide and meat). •Know if the state 
or province you hunt in requires CWD samples to be submitted after harvest and 
before you return home. •Plan accordingly for how to handle an animal if your 
hunt is successful. •Locate meat processors in the state or province where you 
are hunting ahead of time so you can get your carcass processed quickly and 
legally before returning to New York. •If you decide to process your own 
animals, de-boning or quartering deer, elk or moose is easy if you plan ahead 
and have proper equipment. You can find "how to" videos on the internet before 
you go hunting. •If you intend to have a trophy mounted, you will need to know 
how to prepare the hide, cape and antlers to eliminate potentially infectious 
CWD material. •Proper handling of wild meat and the trophy will eliminate all 
the prohibited parts required by New York's CWD regulation.
DEC recommends that hunters dispose of any cervid carcass waste, even from 
New York deer, into a proper waste stream either by putting butcher scrap in 
with household trash or otherwise ensuring it ends up in a licensed landfill. 
Landowners may dispose of their own deer on their property, but it is illegal in 
all cases for deer cutters (meat processors/butchers) and taxidermists to 
dispose of waste generated from their business in any way other than a landfill 
or rendering facility.
DEC also recommends that people not use real deer urine-based lures because 
CWD can be transmitted through infected deer urine. Deer urine, used in 
commercial lures or scents, originates from captive deer on deer farms. In many 
cases, the urine from multiple deer farms is combined for commercial use. If 
there are CWD prions in the urine-based product it can contaminate the soil and 
potentially spread CWD to deer in that hunting area. If healthy animals ingest 
enough infectious CWD material, it could result in the establishment or spread 
of the disease. There are proven synthetic deer lure alternatives available on 
the market.
Every year hunters in New York are found in possession of deer or other 
cervid carcasses taken out-of-state. Many of these were imported illegally. 
Bringing in animals from CWD positive states or provinces and discarding the 
scrap on the landscape increases the risk that CWD will become re-established in 
New York.
This disease threatens the deer herd for every hunter and could jeopardize 
the quality of the hunting experience forever. In some states where the disease 
is well established, deer herds are experiencing infection rates as high as 50 
percent in older age bucks and nearly 30 percent in the overall herd. New York 
is fortunate that CWD was not verified in any additional deer since the initial 
discovery in Oneida County in 2005. DEC remains vigilant about keeping CWD out 
of the state and continues to monitor the latest science about the disease to 
help keep New York's herds healthy.
For more information about CWD and the latest news on the disease, visit 
the DEC's website or the Chronic Wasting Disease Alliance's web site in the 
right column. 
For Release: Friday, February 1, 2013
DEC Adopts Chronic Wasting Disease Regulations in Response to Pennsylvania 
Discovery
The New York State Department of Environmental Conservation (DEC) has 
adopted changes to its Chronic Wasting Disease (CWD) regulations that prohibit 
people from importing into New York state certain parts of white-tailed deer or 
elk taken in the state of Pennsylvania, DEC Commissioner Joe Martens announced 
today. This revision finalizes the emergency rule implemented last 
October.
The first case of CWD in the state of Pennsylvania was confirmed by the 
Pennsylvania Department of Agriculture last fall. In response, DEC implemented 
an emergency rule to protect New York's valuable wild white-tail deer population 
by prohibiting the importation of the following parts of hunter-killed deer or 
elk taken in Pennsylvania: brain, eyes, spinal cord, tonsils, intestinal tract, 
spleen or retropharyngeal lymph nodes.
"As is the case with many other states where CWD has been identified, 
hunters who take a deer or elk in Pennsylvania must remove the prohibited parts 
before entering New York state," DEC Commissioner Martens said. "Most successful 
hunters will opt to butcher a deer or elk and put the meat in a cooler before 
traveling back to New York."
DEC has conducted an extensive surveillance program since CWD was first 
confirmed in New York in 2005 and has not discovered any additional cases of CWD 
since then. CWD is a contagious neurological disease affecting deer, elk and 
moose. It causes a characteristic spongy degeneration of the brains of infected 
animals resulting in emaciation, abnormal behavior, loss of bodily functions and 
death.
It is not known exactly how CWD is transmitted. The infectious agent may be 
passed from animal to animal through feces, urine or saliva. The minimal 
incubation period between infection and development of the clinical disease 
appears to be about 16 months. The maximum incubation period is unknown, as is 
the point at which shedding of the CWD agent begins during the prolonged course 
of infection.
The movement of infectious material may be one route of transmission. This 
amendment to the CWD regulations will prohibit the importation of those parts of 
a deer or elk where the disease is most likely to be found. While the exact 
health risks of consuming meat from an animal infected with CWD are unknown, DEC 
advises hunters not to consume the meat of any animal that acts abnormal and to 
exercise precautions when butchering animals, such as using rubber or latex 
gloves.
Additional information about CWD and New York's CWD Regulation can be found 
on DEC's website. 
PART 189: CHRONIC WASTING DISEASE
Status of CWD
No new Chronic Wasting Disease (CWD) cases have been identified in New York 
since 2005.
CWD Timeline in New York
Below are details on the initiation of DEC's CWD surveillance program, 
information on the first case of CWD in New York and actions taken by DEC to 
minimize its spread.
2002
•New York initiated a statewide CWD surveillance program in response to the 
first detection of the disease in western states of North America.
2003
•DEC initiated Part 189: Chronic Wasting Disease regulations to reduce the 
risk of bringing the disease into New York and to minimize its spread if it was 
detected in our state.
2005
•In early April, the first case of CWD was confirmed in five white-tailed 
deer from two captive breeding facilities in Oneida County. •After detection, a 
containment area was imposed around the infected area in Madison and Oneida 
counties (Wildlife Management Unit 6P), with a mandatory deer check for 
harvested deer. •An intensive monitoring program was established by DEC to 
sample deer in the infected area. Monitoring efforts for the month of April 
resulted in testing 290 deer samples from Oneida County, 2 from Madison County 
and 25 from Hamilton County. •In late April, two wild white-tailed deer were 
confirmed to have CWD within the infected area.
2009
•Mandatory testing of deer from the Oneida/Madison county containment area 
ended, with routine testing to continue statewide.
2010
•More than 31,000 wild white-tailed deer were tested statewide from 2002 
through 2010. •In July, the Oneida/Madison containment area was lifted as no new 
cases of CWD were detected 
2005 CWD NEW YORK 
Published Date: 2005-03-31 23:50:00
Subject: PRO/AH/EDR> Chronic wasting disease, cervids - USA (NY) 
Archive Number: 20050331.0932
CHRONIC WASTING DISEASE, CERVIDS - USA (NEW YORK)
***********************************************
A ProMED-mail post <http://www.promedmail.org>
ProMED-mail is a program of the International Society for Infectious 
Diseases <http://www.isid.org>
Date: 31 Mar 2005
From: Kristine Brown brownkr@michigan.gov
Source: NY Dept. of Agriculture press release [edited]
Positive Case of CWD Found in Oneida County Deer
Mandatory Testing Protocols Find CWD in a Captive White-Tailed Doe
-------------------------------------------------
The 1st positive case of chronic wasting disease (CWD) in New York State 
has been confirmed in a white-tailed doe from a captive herd in Oneida County. 
CWD is a transmissible disease that affects the brain and central nervous system 
of deer and elk. There is no evidence that CWD is linked to disease in humans or 
domestic livestock other than deer and elk.
The animal that tested positive for CWD was a 6-year-old white-tailed doe 
that was slaughtered from a captive herd in Oneida County as part of the State's 
mandatory CWD surveillance and testing protocols. Preliminary tests performed at 
the New York State Veterinary Diagnostic Laboratory at Cornell University 
determined the presumptive positive, which was confirmed late yesterday by the 
National Veterinary Services Laboratory in Ames, Iowa. The New York State 
Department of Agriculture and Markets has officially quarantined the index herd 
in which the positive deer was found, and will depopulate and test all deer on 
the premises. Other herds associated with the index herd have also been 
quarantined and an investigation has been initiated to find and test any 
susceptible deer that came into contact with the index herd and to assess the 
health and environmental risks associated with such establishments. The 
Department of Environmental Conservation (DEC) will conduct intensive monitoring 
of the wild deer population surrounding the index herd to ensure CWD has not 
spread to wild deer.
CWD is a transmissible spongiform encephalopathy (TSE) of deer and elk. 
Scientific and epidemiological research into CWD is ongoing. To date, research 
shows that the disease is typified by chronic weight loss, is always fatal, and 
is transmissible between susceptible species. CWD has only been found in members 
of the deer family in North America, which include white-tailed deer, mule deer, 
elk and moose.
CWD has been detected in both wild and captive deer and elk populations in 
isolated regions of North America. To date, CWD has been found in Colorado, 
Illinois, Kansas, Minnesota, Montana, Nebraska, New Mexico, Oklahoma, South 
Dakota, Utah, Wisconsin and Wyoming in the United States, and in Saskatchewan 
and Alberta in Canada.
Establishing the known CWD health status of captive and wild cervid 
populations is a critical component for controlling CWD. In New York, the 
responsibility for controlling CWD is shared between the State Department of 
Agriculture and Markets, DEC, and the U.S. Department of Agriculture's (USDA) 
Animal and Plant Health Inspection Service (APHIS).
New York's cooperative, active surveillance program serves as a model for 
the nation in CWD control. The State Department of Agriculture and Markets 
monitors the health and movement of all captive deer and elk for the presence of 
common livestock diseases, including CWD. In July 2004, the Department initiated 
the CWD Enhanced Surveillance and Monitoring Program, which requires captive 
deer and elk herd owners to take various actions, including routine sampling and 
testing, animal identification and an annual herd inventory. Since the inception 
of testing for CWD in 2000, 681 captive deer and elk have been tested and found 
negative for CWD. DEC issues licenses to individuals who possess, import or sell 
white-tailed deer. DEC also routinely tests New York's wild deer population. 
Following the discovery of CWD in Wisconsin, DEC implemented a statewide 
surveillance program in April 2002 to test wild white-tailed deer for the 
presence of CWD. Samples are collected and sent to an approved USDA laboratory 
for analysis. To date, DEC has taken samples from 3457 wild white-tailed deer, 
including 40 from the county where the positive deer was found. All samples from 
wild white-tailed deer have tested to date have been negative for CWD. DEC will 
also implement precautionary regulations limiting transportation and possession 
of whole carcasses and some parts of wild deer taken near the location of the 
captive herd. These regulations will be similar to those currently in place for 
importation of carcasses and parts of deer into New York.
DEC has also implemented regulations restricting various activities to help 
control CWD within the State, including restrictions on the importation of live 
deer and elk, deer feeding, importation and possession of certain deer parts and 
carcasses, and transportation of deer and elk carcasses through New York 
State.
USDA APHIS supports individual State programs by providing funding for CWD 
prevention and surveillance. USDA APHIS reimburses states conducting CWD testing 
on their wild and captive cervid population and also provides indemnification 
dollars for captive herds that must be destroyed due to the presence of 
CWD.
New York State has 433 establishments raising 9600 deer and elk in 
captivity. In the wild, DEC estimates there are approximately one million deer 
statewide.
--
Kristine Brown
Laboratory Technician
Wildlife Disease Laboratory
Wildlife Division
Michigan Dept. of Natural Resources
brownkr@michigan.gov 
[This is the 1st time CWD has been found in New York State. This is a blow 
to the NY cervid industry. Undoubtedly, in addition to the actions identified in 
the press release, NY will be examining how the positive deer came to be in New 
York State. Was the animal imported from a previously positive region? Was this 
a case of spontaneous disease? The officials will be conducting a very thorough 
investigation. - Mod.TG] 
[ProMEd-mail thanks to A-lan Banks  and 
Terry S. Singeltary Sr.  for submitting newswires 
covering this topic. - Mod.MPP]   
See Also
Chronic wasting disease update 2005 (02) 20050201.0346
Chronic wasting disease update 2005 20050131.0337 2004
----
Chronic wasting disease update 2004 (05) 20041218.3338
Chronic wasting disease update 2004 (04) 20041212.3290 
...................tg/pg/mpp 
Published Date: 2005-05-05 23:50:00 
Subject: PRO/AH/EDR> Chronic wasting disease, cervids - USA (NY)(05) 
Archive Number: 20050505.1241 
 CHRONIC WASTING DISEASE, CERVIDS - USA (NEW YORK)(05) 
***************************************************** 
A ProMED-mail ipost 
ProMED-mail, a program of the International Society for Infectious Diseases 
<http://www.isid.org> 
Date: 4 May 2005 
From: Terry S. Singeltary Sr.   
Source: Official News release, New York State Department of Environmental 
Conservation [edited] 
 The New York State Department of Environmental Conservation today 
announced that it has received the remainder of test results for chronic wasting 
disease (CWD) that were part of intensive sampling efforts in central New York. 
DEC has received 2 positive results for the disease out of 292 wild deer 
sampled. 
The 1st positive result in a wild deer was announced on 27 Apr 2005, and 
came from a yearling white-tailed deer sampled from the Town of Verona, Oneida 
County. The 2nd positive result is from a 3-year-old doe (female), located 
within a mile of the location where the initial positive result was detected. 
The sample tissues were tested at the State's Veterinary Diagnostic Laboratory 
at Cornell University. These are the 1st known occurrences of CWD in wild deer 
in New York State. DEC implemented intensive monitoring efforts after CWD was 
found in 2 captive white-tailed deer herds in Oneida County, the 1st incidents 
of CWD in New York State. On 8 Apr 2005, the State Department of Agriculture and 
Markets (DAM) completed testing of the captive deer and found a total of 5 
positive results for CWD in the 2 captive herds. 
DEC, along with the U.S. Department of Agriculture's Wildlife Services 
program, completed intensive monitoring on 30 Apr 2005. The effort resulted in 
290 samples of wild deer from Oneida County, 2 from neighboring Madison County, 
and 25 wild deer from the Town of Arietta, Hamilton County. Since 2002, DEC has 
conducted statewide sampling of wild deer for CWD. When combined with sampling 
efforts in Oneida and Hamilton Counties, DEC has collected more than 3700 
samples from wild white-tailed deer. 
DEC and DAM will continue public outreach to interested parties in central 
New York to help educate citizens on CWD and to discuss next steps to be taken. 
The agencies will hold a public meeting on Thu 12 May 2005, at 7 p.m. in the 
Vernon-Verona-Sherrill High School Auditorium, located on State Highway 31 in 
the Town of Verona. In addition, DEC and DAM will conduct additional outreach 
and continue to aggressively pursue inspection and enforcement across the State. 
DAM continues to investigate, sample and test white-tailed deer from 2 captive 
herds directly associated with the 2 herds that were confirmed positive for CWD 
in Oneida County. Results for these sampling efforts will be announced when 
available. 
Statewide sampling for CWD -- which has resulted in more than 1000 tests 
each year -- will be increased to closely monitor the distribution and 
prevalence of CWD in wild deer. In addition, DEC has implemented emergency 
regulations regarding the handling, transport and management of deer in the 
State. The emergency regulations are currently in effect and represent an 
aggressive response to the recent discovery of chronic wasting disease (CWD) in 
Oneida County. DEC's emergency regulations are designed to ensure the proper 
handling of deer and prevent further spread of CWD in the wild herd. The 
emergency regulations are effective for 90 days. In addition, DEC will begin the 
process of developing permanent regulations, which will appear in the State 
Register and include a 45-day public comment period. 
CWD is a transmissible disease that affects the brain and central nervous 
system of certain deer and elk. There is no evidence that CWD is linked to 
disease in humans or domestic livestock other than deer and elk. More 
information on CWD can be found at DEC's website at <http://www.dec.state.ny.us/website/dfwmr/wildlife/deer/currentcwd.html> 
For more information contact: Michael Fraser (518) 402-8000 #05-48 -- 
ProMED-mail 
See Also
Chronic wasting disease, cervids - USA (NY)(04) 20050428.1187
Chronic wasting disease, cervids - USA (NY) (03): human exposure 
20050409.1028 
Chronic wasting disease, cervids - USA (NY)(02) 20050402.0952
Chronic wasting disease, cervids - USA (NY) 20050331.0932
.............................tg/pg/jw
##########################################################
*** PRION2013 CONGRESSIONAL ABSTRACTS CWD ***
CWD POTENTIAL TRANSMISSION TO HUMANS SCIENCE
PRION2013 CONGRESSIONAL ABSTRACTS CWD 
Sunday, August 25, 2013
HD.13: CWD infection in the spleen of humanized transgenic mice 
Liuting Qing and Qingzhong Kong 
Case Western Reserve University; Cleveland, OH USA 
Chronic wasting disease (CWD) is a widespread prion disease in free-ranging 
and captive cervid species in North America, and there is evidence suggesting 
the existence of multiple CWD strains. The susceptibility of human CNS and 
peripheral organs to the various CWD prion strains remains largely unclear. 
Current literature suggests that the classical CWD strain is unlikely to infect 
human brain, but the potential for peripheral infection by CWD in humans is 
unknown. We detected protease-resistant PrpSc in the spleens of a few humanized 
transgenic mice that were intracerebrally inoculated with natural CWD isolates, 
but PrpSc was not detected in the brains of any of the CWD-inoculated mice. Our 
ongoing bioassays in humanized Tg mice indicate that intracerebral challenge 
with such PrpSc-positive humanized mouse spleen already led to prion disease in 
most animals. 
***These results indicate that the CWD prion may have the potential to 
infect human peripheral lymphoid tissues. 
Oral.15: Molecular barriers to zoonotic prion transmission: Comparison of 
the ability of sheep, cattle and deer prion disease isolates to convert normal 
human prion protein to its pathological isoform in a cell-free system 
Marcelo A.Barria,1 Aru Balachandran,2 Masanori Morita,3 Tetsuyuki 
Kitamoto,4 Rona Barron,5 Jean Manson,5 Richard Kniqht,1 James W. lronside1 and 
Mark W. Head1 
1National CJD Research and Surveillance Unit; Centre for Clinical Brain 
Sciences; School of Clinical Sciences; The University of Edinburgh; Edinburgh, 
UK; 2National and OIE Reference Laboratory for Scrapie and CWD; Canadian Food 
Inspection Agency; Ottawa Laboratory; Fallowfield. ON Canada; 3Infectious 
Pathogen Research Section; Central Research Laboratory; Japan Blood Products 
Organization; Kobe, Japan; 4Department of Neurological Science; Tohoku 
University Graduate School of Medicine; Sendai. Japan; 5Neurobiology Division; 
The Roslin Institute and R(D)SVS; University of Edinburgh; Easter Bush; 
Midlothian; Edinburgh, UK 
Background. Bovine spongiform encephalopathy (BSE) is a known zoonotic 
prion disease, resulting in variant Creurzfeldt- Jakob disease (vCJD) in humans. 
In contrast, classical scrapie in sheep is thought to offer little or no danger 
to human health. However, a widening range of prion diseases have been 
recognized in cattle, sheep and deer. The risks posed by individual animal prion 
diseases to human health cannot be determined a priori and are difficult to 
assess empirically. The fundamemal event in prion disease pathogenesis is 
thought to be the seeded conversion of normal prion protein (PrPC) to its 
pathological isoform (PrPSc). Here we report the use of a rapid molecular 
conversion assay to test whether brain specimens from different animal prion 
diseases are capable of seeding the conversion of human PrPC ro PrPSc. 
Material and Methods. Classical BSE (C-type BSE), H-type BSE, L-type BSE, 
classical scrapie, atypical scrapie, chronic wasting disease and vCJD brain 
homogenates were tested for their ability to seed conversion of human PrPC to 
PrPSc in protein misfolding cyclic amplification (PMCA) reactions. Newly formed 
human PrPSc was detected by protease digestion and western blotting using the 
antibody 3F4. 
Results. C-type BSE and vCJD were found to efficiently convert PrPC to 
PrPSc. Scrapie failed to convert human PrPC to PrPSc. Of the other animal prion 
diseases tested only chronic wasting disease appeared to have the capability ro 
convert human PrPC to PrPSc. The results were consistent whether the human PrPC 
came from human brain, humanised transgenic mouse brain or from cultured human 
cells and the effect was more pronounced for PrPC with methionine at codon 129 
compared with that with valine. 
Conclusion. Our results show that none of the tested animal prion disease 
isolates are as efficient as C-type BSE and vCJD in converting human prion 
protein in this in vitro assay. 
***However, they also show that there is no absolute barrier ro conversion 
of human prion protein in the case of chronic wasting disease. 
PRION2013 CONGRESSIONAL ABSTRACTS CWD 
Sunday, August 25, 2013 
***Chronic Wasting Disease CWD risk factors, humans, domestic cats, blood, 
and mother to offspring transmission
Sunday, July 21, 2013 
*** As Chronic Wasting Disease CWD rises in deer herd, what about risk for 
humans? 
PRION2013 CONGRESSIONAL ABSTRACTS CWD 
Tuesday, September 17, 2013 
Mother to Offspring Transmission of Transmissible Spongiform Encephalopathy 
TSE prion disease 
Thursday, August 08, 2013 
Characterization of the first case of naturally occurring chronic wasting 
disease in a captive red deer (Cervus elaphus) in North America
Wednesday, September 04, 2013 
***cwd - cervid captive livestock escapes, loose and on the run in the 
wild... 
Tuesday, September 10, 2013 
Review and Updates of the USDA-APHIS Veterinary Services (VS) National 
Chronice Wasting Disease (CWD) Program 2012-2013 
Sunday, September 01, 2013 
hunting over gut piles and CWD TSE prion disease 
THIS IS NOT GOOD... 
Uptake of Prions into Plants 
Prion2013 
Friday, August 09, 2013 
***CWD TSE prion, plants, vegetables, and the potential for environmental 
contamination
Thursday, July 11, 2013 
The New Hornographers: The Fight Over the Future of Texas Deer, Captive 
shooting pens, and the CWD TSE prion disease 
Thursday, October 03, 2013 
TAHC ADOPTS CWD RULE THAT the amendments _REMOVE_ the requirement for a 
specific fence height for captives 
Texas Animal Health Commission (TAHC) ANNOUNCEMENT October 3, 2013 
TEXAS CWD STATUS 2001 – 2002 email snips to TAHC...tss
Captive Cervids
There have been no reported CWD infections of captive elk or deer in Texas. 
There is currently no mandatory surveillance program for susceptible cervids 
kept on game farms, although, there has been voluntary surveillance since 1999, 
which requires owners of participating herds to maintain an annual herd 
inventory and submit samples for all mortalities of animals over 16 months of 
age. 
snip... 
SO, i thought i would just see where these Ecoregions were, and just how 
the CWD testing was distributed. YOU would think that with the cluster of CWD 
bordering TEXAS at the WPMR in NM, you would have thought this would be where 
the major CWD testing samples were to have been taken? wrong! let's have a look 
at the sample testing. here is map of CWD in NM WPMR bordering TEXAS; 
NEW MEXICO 7 POSITIVE CWD WHITE SANDS MISSILE RANGE MAP 
NEXT, let's have a look at the overall distribution of CWD in Free-Ranging 
Cervids and see where the CWD cluster in NM WSMR borders TEXAS; 
Current Distribution of Chronic Wasting Disease in Free-Ranging Cervids 
NOW, the MAP of the Exoregion where the samples were taken to test for CWD; 
CWD SURVEILLANCE SAMPLE SUBMISSIONS TEXAS
Ecoregions of TEXAS
IF you look at the area around the NM WSMR where the CWD cluster was and 
where it borders TEXAS, that ecoregion is called Trans Pecos region. Seems if my 
Geography and my Ciphering is correct ;-) that region only tested 55% of it's 
goal. THE most important area on the MAP and they only test some 96 samples, 
this in an area that has found some 7 positive animals? NOW if we look at the 
only other border where these deer from NM could cross the border into TEXAS, 
this area is called the High Plains ecoregion, and again, we find that the 
sampling for CWD was pathetic. HERE we find that only 9% of it's goal of CWD 
sampling was met, only 16 samples were tested from some 175 that were suppose to 
be sampled.
AS i said before; 
> SADLY, they have not tested enough from the total population to
> know if CWD is in Texas or not. 
BUT now, I will go one step further and state categorically that they are 
not trying to find it. just the opposite it seems, they are waiting for CWD to 
find them, as with BSE/TSE in cattle, and it will eventually... 
snip...see full text ; 
snip... 
Monday, February 11, 2013
TEXAS CHRONIC WASTING DISEASE CWD Four New Positives Found in Trans 
Pecos
Tuesday, July 10, 2012 
Chronic Wasting Disease Detected in Far West Texas 
Monday, March 26, 2012
Texas Prepares for Chronic Wasting Disease CWD Possibility in Far West 
Texas
Monday, March 26, 2012
3 CASES OF CWD FOUND NEW MEXICO MULE DEER SEVERAL MILS FROM TEXAS 
BORDER
Saturday, October 19, 2013 
ACA Council Meets to Endorse Several Proposed USAHA Resolutions (CWD TSE 
PRION DISEASE) 
Wednesday, August 21, 2013 
IOWA DNR EMERGENCY CONSENT ORDER IN THE MATTER OF TOM & LINDA BRAKKE 
D/B/A PINE RIDGE HUNTING LODGE UPDATE AUGUST 21, 2013 
Sunday, January 06, 2013 
USDA TO PGC ONCE CAPTIVES ESCAPE 
*** "it‘s no longer its business.” 
Saturday, June 29, 2013 
PENNSYLVANIA CAPTIVE CWD INDEX HERD MATE YELLOW *47 STILL RUNNING LOOSE IN 
INDIANA, YELLOW NUMBER 2 STILL MISSING, AND OTHERS ON THE RUN STILL IN LOUISIANA 
Monday, June 24, 2013 
The Effects of Chronic Wasting Disease on the Pennsylvania Cervid Industry 
Following its Discovery 
Tuesday, June 11, 2013 
CWD GONE WILD, More cervid escapees from more shooting pens on the loose in 
Pennsylvania 
Tuesday, May 28, 2013 
Chronic Wasting Disease CWD quarantine Louisiana via CWD index herd 
Pennsylvania Update May 28, 2013 
6 doe from Pennsylvania CWD index herd still on the loose in Louisiana, 
quarantine began on October 18, 2012, still ongoing, Lake Charles premises. 
October 16, 2013 
Pennsylvania Adjusts CWD Rules 
Monday, October 07, 2013 
The importance of localized culling in stabilizing chronic wasting disease 
prevalence in white-tailed deer populations 
Monday, October 21, 2013 
Current CWD Status WHHCC Meeting – 5-6 February 2013
MAD COW TESTING ONLY CATCHES SOME MAD COWS 
SPREADING IT ALL AROUND
Saturday, October 19, 2013 
***A comparative study of modified confirmatory techniques and additional 
immuno-based methods for non-conclusive autolytic Bovine spongiform 
encephalopathy cases 
Wednesday, September 25, 2013 
Inspections, Compliance, Enforcement, and Criminal Investigations BSE TSE 
PRION 2013 
Wednesday, October 09, 2013 
WHY THE UKBSEnvCJD ONLY THEORY IS SO POPULAR IN IT'S FALLACY, £41,078,281 
in compensation REVISED
Thursday, October 10, 2013 
*** CJD REPORT 1994 increased risk for consumption of veal and venison and 
lamb ***
Monday, October 14, 2013 
Researchers estimate one in 2,000 people in the UK carry variant CJD 
proteins 
Sunday, August 11, 2013
Creutzfeldt-Jakob Disease CJD cases rising North America updated report 
August 2013
Creutzfeldt-Jakob Disease CJD cases rising North America with Canada seeing 
an extreme increase of 48% between 2008 and 2010
Friday, August 16, 2013
*** Creutzfeldt-Jakob disease (CJD) biannual update August 2013 U.K. and 
Contaminated blood products induce a highly atypical prion disease devoid of 
PrPres in primates
Sunday, September 08, 2013
Iatrogenic Creutzfeldt-Jakob disease via surgical instruments and 
decontamination possibilities for the TSE prion
Wednesday, September 25, 2013 
Cleaning, disinfection and sterilization of surface prion contamination 
*** The potential impact of prion diseases on human health was greatly 
magnified by the recognition that interspecies transfer of BSE to humans by beef 
ingestion resulted in vCJD. While changes in animal feed constituents and 
slaughter practices appear to have curtailed vCJD, there is concern that CWD of 
free-ranging deer and elk in the U.S. might also cross the species barrier. 
Thus, consuming venison could be a source of human prion disease. Whether BSE 
and CWD represent interspecies scrapie transfer or are newly arisen prion 
diseases is unknown. Therefore, the possibility of transmission of prion disease 
through other food animals cannot be ruled out. There is evidence that vCJD can 
be transmitted through blood transfusion. There is likely a pool of unknown size 
of asymptomatic individuals infected with vCJD, and there may be asymptomatic 
individuals infected with the CWD equivalent. These circumstances represent a 
potential threat to blood, blood products, and plasma supplies. 
Wednesday, October 23, 2013
Steve Lightfoot: West Texas Mule Deer rules CWD Management Plan mandatory check stations for harvested mule deer taken inside the CWD Containment Zone
Steve Lightfoot: West Texas Mule Deer rules 
Steve Lightfoot, Texas Parks and Wildlife Department, guest columnist 
San Angelo Standard Times 
Posted October 23, 2013 at 2:35 p.m. 
Rick Meritt harvested this Mule deer in West Texas last year. Photo used 
with permission, Steve Alderman and Rick Meritt. www.muledeercountry.com. See 
the original posting at 
http://muledeercountry.com/forum/desert-mule-deer/texas/. 
muledeercountry.com
Rick Meritt harvested this Mule deer in West Texas last year. Photo used 
with permission, Steve Alderman and Rick Meritt. www.muledeercountry.com. See 
the original posting at http://muledeercountry.com/forum/desert-mule-deer/texas/.
Wildlife officials are reminding mule deer hunters and landowners in far 
West Texas about the protocols developed as part of Texas Parks and Wildlife 
Department’s (TPWD) Chronic Wasting Disease management plan. The plan includes 
mandatory check stations for harvested mule deer taken inside the CWD 
Containment Zone, which covers portions of Hudspeth, Culberson, and El Paso 
counties. See map of CWD zones at http://www.tpwd.state.tx.us/cwd.
The management plan was implemented after CWD was detected in tissue 
samples from two mule deer in far West Texas during the summer of 2012. Those 
were the first cases of CWD detected in Texas deer.
Nearly 300 tissue samples were collected from hunter harvested mule deer 
from the Trans Pecos ecoregion during the 2012-13 season for CWD testing. Texas 
A&M Veterinary Medical Diagnostic Laboratory and National Veterinary 
Services Laboratories (NVSL) confirmed CWD in four of those samples. All 
CWD-positive deer were harvested within the CWD Containment Zone.
Of 298 deer sampled during last hunting season, 107 were harvested in the 
Containment Zone, 93 were harvested in the adjacent High Risk Zone, 25 were 
harvested in the Buffer Zone, and 73 deer were harvested outside of the CWD 
zones. Nineteen of the samples collected from the Containment Zone were from 
deer harvested in the Hueco Mountains.
Hunters taking mule deer inside the Containment Zone during the 2013 
general mule deer hunting season, Nov. 22 – Dec. 8, are required to submit their 
harvest (unfrozen head) for CWD sampling at mandatory check stations within 24 
hours of harvest.
“We recommend hunters in the Containment Zone and High Risk Zone quarter 
deer in the field and leave all but the quarters, backstraps, and head at the 
site of harvest if it is not possible to bury the inedible carcass parts at 
least 6 feet deep on the ranch or take them to a landfill,” said Shawn Gray, 
Mule Deer Program Leader for TPWD.
Mandatory check stations will be open from 9 a.m. to 9 p.m. Nov. 22 – Dec. 
9. Stations will be located in Cornudas at May’s Café (on US 62-180) and in Van 
Horn at Van Horn Convention Center (1801 West Broadway).
Hunters who harvest deer in the Containment Zone outside the general season 
under the authority of MLDP (Managed Lands Deer Permits) will need to call TPWD 
at (512) 221-8491 the day the deer is harvested to make arrangements to have the 
deer sampled for CWD.
In addition to protocols within the Containment Zone, TPWD has established 
check stations for voluntary CWD sampling for deer harvested in other parts of 
West Texas. Biologists have been collecting mule deer harvest data in the region 
since 1980 and this year CWD sampling will be offered in addition to age and 
weight measurements.
Voluntary check stations will be established at the following locations 
during the first three weekends of the general season, Saturday through Monday 
(Nov. 23–25, Nov. 30–Dec. 2 and Dec. 6–8), from 9 a.m. – 5 p.m. Saturday and 
Sunday and 9 a.m. – 1 p.m. Monday:
Midland at Naturally Fresh (Deer Processor) (1501 Elwyn)
Bakersfield at Chevron Station (south of I10; Exit 294)
Sanderson at Slim’s Auto Repair (823 West Oak; Intersection of US 90 and 
285)
Alpine at Hip-O Taxidermy (east side of town on US 90, across from Dairy 
Queen)
All deer brought to the check stations this season will be aged as part of 
our CWD surveillance. Additional biological information such as antler 
measurements and field dressed weights will also be collected as time 
allows.
TPWD has tested almost 30,000 wild hunter-harvested and road-killed deer in 
Texas since 2002. The captive-deer industry in Texas has submitted more than 
7,400 CWD test results as well.
“CWD has not been detected anywhere outside of the Hueco Mountains,” said 
Mitch Lockwood, Big Game Program Director with TPWD. “But adequate surveillance 
in that part of West Texas depends on check stations and we appreciate the 
cooperation and active participation of hunters and landowners in this area. 
Saturday, October 19, 2013 
ACA Council Meets to Endorse Several Proposed USAHA Resolutions (CWD TSE 
PRION DISEASE) 
Thursday, October 03, 2013 
TAHC ADOPTS CWD RULE THAT the amendments _REMOVE_ the requirement for a 
specific fence height for captives 
Texas Animal Health Commission (TAHC) 
ANNOUNCEMENT
October 3, 2013 
Thursday, July 04, 2013 
New TAHC Movement Requirements for Species Susceptible to Chronic Wasting 
Disease (CWD) 
Date: Sun, 25 Aug 2002 19:45:14 –0500
TEXAS OLD STATISTICS BELOW FOR PAST CWD TESTING; 
Subject: CWD testing in Texas
Date: Sun, 25 Aug 2002 19:45:14 –0500
From: Kenneth Waldrup
To: flounder@wt.net
CC: mcoats@tahc.state.tx.us
Dear Dr. Singletary,
In Fiscal Year 2001, seven deer from Texas were tested by the National 
Veterinary Services Laboratory (NVSL) for CWD (5 fallow deer and 2 white-tailed 
deer). In Fiscal Year 2002, seven elk from Texas were tested at NVSL (no deer). 
During these two years, an additional six elk and one white-tailed deer were 
tested at the Texas Veterinary Medical Diagnostic Laboratory (TVMDL). In Fiscal 
Year 2002, four white-tailed deer (free-ranging clinical suspects) and at least 
eight other white-tailed deer have been tested at TVMDL. One elk has been tested 
at NVSL. All of these animals have been found negative for CWD. Dr. Jerry Cooke 
of the Texas Parks and Wildlife Department also has records of 601 clinically 
ill white-tailed deer which were necropsied at Texas A&M during the late 
1960's and early 1970's, and no spongiform encepalopathies were noted.
Thank you for your consideration.
Ken Waldrup, DVM, PhD Texas Animal Health Commission
========================
TEXAS CWD STATUS
Captive Cervids
There have been no reported CWD infections of captive elk or deer in Texas. 
There is currently no mandatory surveillance program for susceptible cervids 
kept on game farms, although, there has been voluntary surveillance since 1999, 
which requires owners of participating herds to maintain an annual herd 
inventory and submit samples for all mortalities of animals over 16 months of 
age. 
snip... 
SO, i thought i would just see where these Ecoregions were, and just how 
the CWD testing was distributed. YOU would think that with the cluster of CWD 
bordering TEXAS at the WPMR in NM, you would have thought this would be where 
the major CWD testing samples were to have been taken? wrong! let's have a look 
at the sample testing. here is map of CWD in NM WPMR bordering TEXAS; 
NEW MEXICO 7 POSITIVE CWD WHITE SANDS MISSILE RANGE MAP 
NEXT, let's have a look at the overall distribution of CWD in Free-Ranging 
Cervids and see where the CWD cluster in NM WSMR borders TEXAS; 
Current Distribution of Chronic Wasting Disease in Free-Ranging Cervids 
NOW, the MAP of the Exoregion where the samples were taken to test for 
CWD;
CWD SURVEILLANCE SAMPLE SUBMISSIONS TEXAS
Ecoregions of TEXAS
IF you look at the area around the NM WSMR where the CWD cluster was and 
where it borders TEXAS, that ecoregion is called ***Trans Pecos region. Seems if my 
Geography and my Ciphering is correct ;-) that region only tested 55% of it's 
goal. THE most important area on the MAP and they only test some 96 samples, 
this in an area that has found some 7 positive animals? NOW if we look at the 
only other border where these deer from NM could cross the border into TEXAS, 
this area is called the High Plains ecoregion, and again, we find that the 
sampling for CWD was pathetic. HERE we find that only 9% of it's goal of CWD 
sampling was met, only 16 samples were tested from some 175 that were suppose to 
be sampled.
AS i said before; 
> SADLY, they have not tested enough from the total population to
> know if CWD is in Texas or not. 
BUT now, I will go one step further and state categorically that they are 
not trying to find it. just the opposite it seems, they are waiting for CWD to 
find them, as with BSE/TSE in cattle, and it will eventually... 
snip...see full text ; 
snip...
Monday, February 11, 2013
TEXAS CHRONIC WASTING DISEASE CWD Four New Positives Found in Trans 
Pecos
Tuesday, July 10, 2012 
Chronic Wasting Disease Detected in Far West Texas 
Monday, March 26, 2012
Texas Prepares for Chronic Wasting Disease CWD Possibility in Far West 
Texas
Monday, March 26, 2012
3 CASES OF CWD FOUND NEW MEXICO MULE DEER SEVERAL MILS FROM TEXAS 
BORDER
Wednesday, August 21, 2013 
IOWA DNR EMERGENCY CONSENT ORDER IN THE MATTER OF TOM & LINDA BRAKKE 
D/B/A PINE RIDGE HUNTING LODGE UPDATE AUGUST 21, 2013 
Wednesday, September 04, 2013 
***cwd - cervid captive livestock escapes, loose and on the run in the 
wild... 
Sunday, January 06, 2013 
USDA TO PGC ONCE CAPTIVES ESCAPE 
*** "it‘s no longer its business.” 
Saturday, June 29, 2013 
PENNSYLVANIA CAPTIVE CWD INDEX HERD MATE YELLOW *47 STILL RUNNING LOOSE IN 
INDIANA, YELLOW NUMBER 2 STILL MISSING, AND OTHERS ON THE RUN STILL IN LOUISIANA 
Monday, June 24, 2013 
The Effects of Chronic Wasting Disease on the Pennsylvania Cervid Industry 
Following its Discovery 
Tuesday, June 11, 2013 
CWD GONE WILD, More cervid escapees from more shooting pens on the loose in 
Pennsylvania 
Tuesday, May 28, 2013 
Chronic Wasting Disease CWD quarantine Louisiana via CWD index herd 
Pennsylvania Update May 28, 2013 
6 doe from Pennsylvania CWD index herd still on the loose in Louisiana, 
quarantine began on October 18, 2012, still ongoing, Lake Charles premises. 
Thursday, August 08, 2013 
Characterization of the first case of naturally occurring chronic wasting 
disease in a captive red deer (Cervus elaphus) in North America 
Thursday, July 11, 2013 
The New Hornographers: The Fight Over the Future of Texas Deer, Captive 
shooting pens, and the CWD TSE prion disease 
Friday, August 09, 2013 
CWD TSE prion, plants, vegetables, and the potential for environmental 
contamination
Friday, September 27, 2013 
***Uptake of Prions into Plants 
Presentation Abstract 
Tuesday, September 17, 2013 
Mother to Offspring Transmission of Transmissible Spongiform Encephalopathy 
TSE prion disease 
Sunday, September 01, 2013 
hunting over gut piles and CWD TSE prion disease 
Thursday, May 31, 2012 
CHRONIC WASTING DISEASE CWD PRION2012 Aerosol, Inhalation transmission, 
Scrapie, cats, species barrier, burial, and more 
Monday, August 8, 2011 
Susceptibility of Domestic Cats to CWD Infection 
Friday, November 09, 2012 
*** Chronic Wasting Disease CWD in cervidae and transmission to other 
species 
Sunday, November 11, 2012 
*** Susceptibilities of Nonhuman Primates to Chronic Wasting Disease 
November 2012 
Friday, December 14, 2012 
Susceptibility Chronic Wasting Disease (CWD) in wild cervids to Humans 2005 
- December 14, 2012 
Sunday, August 25, 2013 
Prion2013 Chronic Wasting Disease CWD risk factors, humans, domestic cats, 
blood, and mother to offspring transmission
NOW, let’s take a look at what the science is saying on the risk factors of 
human TSE prion disease from CWD prion disease of cervids. 
first, from the cdc/nih et al prion gods, and what they said on human cwd 
potential, and what that might look like ; 
now, let’s see what the authors said about this casual link, personal 
communications years ago. see where it is stated NO STRONG evidence. so, does 
this mean there IS casual evidence ???? 
“Our conclusion stating that we found no strong evidence of CWD 
transmission to humans” 
From: TSS (216-119-163-189.ipset45.wt.net) 
Subject: CWD aka MAD DEER/ELK TO HUMANS ??? 
Date: September 30, 2002 at 7:06 am PST 
From: "Belay, Ermias" 
To: 
Cc: "Race, Richard (NIH)" ; ; "Belay, Ermias" 
Sent: Monday, September 30, 2002 9:22 AM 
Subject: RE: TO CDC AND NIH - PUB MED- 3 MORE DEATHS - CWD - YOUNG HUNTERS 
Dear Sir/Madam, 
In the Archives of Neurology you quoted (the abstract of which was attached 
to your email), we did not say CWD in humans will present like variant 
CJD.
That assumption would be wrong. I encourage you to read the whole article 
and call me if you have questions or need more clarification (phone: 
404-639-3091). Also, we do not claim that "no-one has ever been infected with 
prion disease from eating venison." Our conclusion stating that we found no 
strong evidence of CWD transmission to humans in the article you quoted or in 
any other forum is limited to the patients we investigated. 
Ermias Belay, M.D. Centers for Disease Control and Prevention 
-----Original Message----- 
From: 
Sent: Sunday, September 29, 2002 10:15 AM 
To: rr26k@nih.gov; rrace@niaid.nih.gov; ebb8@CDC.GOV 
Subject: TO CDC AND NIH - PUB MED- 3 MORE DEATHS - CWD - YOUNG HUNTERS 
Sunday, November 10, 2002 6:26 PM ......snip........end..............TSS 
Thursday, April 03, 2008 
A prion disease of cervids: Chronic wasting disease 
2008 1: Vet Res. 2008 Apr 3;39(4):41 
A prion disease of cervids: Chronic wasting disease 
Sigurdson CJ. 
snip... 
*** twenty-seven CJD patients who regularly consumed venison were reported 
to the Surveillance Center***, 
snip... 
full text ; 
Monday, February 09, 2009
Exotic Meats USA Announces Urgent Statewide Recall of Elk Tenderloin 
Because It May Contain Meat Derived From An Elk Confirmed To Have CWD 
snip... 
Cross-sequence transmission of sporadic Creutzfeldt-Jakob disease creates a 
new prion strain
Date: August 25, 2007 at 12:42 pm PST
our results raise the possibility that CJD cases classified as VV1 may 
include cases caused by iatrogenic transmission of sCJD-MM1 prions or food-borne 
infection by type 1 prions from animals, e.g., chronic wasting disease prions in 
cervid. In fact, two CJD-VV1 patients who hunted deer or consumed venison have 
been reported (40, 41). The results of the present study emphasize the need for 
traceback studies and careful re-examination of the biochemical properties of 
sCJD-VV1 prions. 
Wednesday, March 18, 2009 
Noah's Ark Holding, LLC, Dawson, MN RECALL Elk products contain meat 
derived from an elk confirmed to have CWD NV, CA, TX, CO, NY, UT, FL, OK RECALLS 
AND FIELD CORRECTIONS: FOODS CLASS II 
CWD TO HUMAN RISK FACTORS PRION2013 
PRION2013 CONGRESSIONAL ABSTRACTS 
HD.13: CWD infection in the spleen of humanized transgenic mice 
Liuting Qing and Qingzhong Kong 
Case Western Reserve University; Cleveland, OH USA 
Chronic wasting disease (CWD) is a widespread prion disease in free-ranging 
and captive cervid species in North America, and there is evidence suggesting 
the existence of multiple CWD strains. The susceptibility of human CNS and 
peripheral organs to the various CWD prion strains remains largely unclear. 
Current literature suggests that the classical CWD strain is unlikely to infect 
human brain, but the potential for peripheral infection by CWD in humans is 
unknown. We detected protease-resistant PrpSc in the spleens of a few humanized 
transgenic mice that were intracerebrally inoculated with natural CWD isolates, 
but PrpSc was not detected in the brains of any of the CWD-inoculated mice. Our 
ongoing bioassays in humanized Tg mice indicate that intracerebral challenge 
with such PrpSc-positive humanized mouse spleen already led to prion disease in 
most animals. ***These results indicate that the CWD prion may have the 
potential to infect human peripheral lymphoid tissues. 
===== 
Oral.15: Molecular barriers to zoonotic prion transmission: Comparison of 
the ability of sheep, cattle and deer prion disease isolates to convert normal 
human prion protein to its pathological isoform in a cell-free system 
Marcelo A.Barria,1 Aru Balachandran,2 Masanori Morita,3 Tetsuyuki 
Kitamoto,4 Rona Barron,5 Jean Manson,5 Richard Kniqht,1 James W. lronside1 and 
Mark W. Head1 
1National CJD Research and Surveillance Unit; Centre for Clinical Brain 
Sciences; School of Clinical Sciences; The University of Edinburgh; Edinburgh, 
UK; 2National and OIE Reference Laboratory for Scrapie and CWD; Canadian Food 
Inspection Agency; Ottawa Laboratory; Fallowfield. ON Canada; 3Infectious 
Pathogen Research Section; Central Research Laboratory; Japan Blood Products 
Organization; Kobe, Japan; 4Department of Neurological Science; Tohoku 
University Graduate School of Medicine; Sendai. Japan; 5Neurobiology Division; 
The Roslin Institute and R(D)SVS; University of Edinburgh; Easter Bush; 
Midlothian; Edinburgh, UK 
Background. Bovine spongiform encephalopathy (BSE) is a known zoonotic 
prion disease, resulting in variant Creurzfeldt- Jakob disease (vCJD) in humans. 
In contrast, classical scrapie in sheep is thought to offer little or no danger 
to human health. However, a widening range of prion diseases have been 
recognized in cattle, sheep and deer. The risks posed by individual animal prion 
diseases to human health cannot be determined a priori and are difficult to 
assess empirically. The fundamemal event in prion disease pathogenesis is 
thought to be the seeded conversion of normal prion protein (PrPC) to its 
pathological isoform (PrPSc). Here we report the use of a rapid molecular 
conversion assay to test whether brain specimens from different animal prion 
diseases are capable of seeding the conversion of human PrPC ro PrPSc. 
Material and Methods. Classical BSE (C-type BSE), H-type BSE, L-type BSE, 
classical scrapie, atypical scrapie, chronic wasting disease and vCJD brain 
homogenates were tested for their ability to seed conversion of human PrPC to 
PrPSc in protein misfolding cyclic amplification (PMCA) reactions. Newly formed 
human PrPSc was detected by protease digestion and western blotting using the 
antibody 3F4. 
Results. C-type BSE and vCJD were found to efficiently convert PrPC to 
PrPSc. Scrapie failed to convert human PrPC to PrPSc. Of the other animal prion 
diseases tested only chronic wasting disease appeared to have the capability ro 
convert human PrPC to PrPSc. The results were consistent whether the human PrPC 
came from human brain, humanised transgenic mouse brain or from cultured human 
cells and the effect was more pronounced for PrPC with methionine at codon 129 
compared with that with valine. 
Conclusion. Our results show that none of the tested animal prion disease 
isolates are as efficient as C-type BSE and vCJD in converting human prion 
protein in this in vitro assay. ***However, they also show that there is no 
absolute barrier ro conversion of human prion protein in the case of chronic 
wasting disease. 
===== 
Invited.16: Studies of chronic wasting disease transmission in cervid and 
non-cervid species 
Edward A, Hoover,1 Candace K. Mathiason,1 Davin M. Henderson,1 Nicholas J. 
Haley,1 Davis M. Seelig,1 Nathaniel D. Denkers,1 Amy V. Nalls,1 Mark D. Zabe,1 
Glenn C. Telling,1 Fernando Goni2 and Thomas Wisniewski,2 
1Prion Research Center; Colorado State University; Fort Collins, CO USA; 
2New York University School of Medicine; New York, NY USA 
How and why some misfolded proteins become horizontally transmitted agents 
and occasionally cross species barriers are issues fundamental to understanding 
prion disease. Chronic wasting disease (CWD) of cervids is perhaps a prototype 
of horizontal prion transmission, encompassing efficient mucosal uptake, 
lymphoid amplification, neuroinvasion, peripheralization, and dissemination via 
mucosal excretion. Efficient mucosal transmission of CWD in deer has been 
demonstrated by oral, nasal, aerosol, and indirect contact exposure. In 
addition, other studies (Mathiason CK, et al.) reported at the symposium support 
a significant role for pre- and/or postnatal transmission of CWD from doe to 
offspring. Accumulating, yet still incomplete, evidence also suggests that the 
period of relatively covert CWD infection may be longer than originally thought. 
Given the above, minimally invasive sensitive assays based on body fluids from 
live animals would aid substantially in understanding the biology of CWD. We 
have been applying seeded realtirne quaking-induced amplification of recombinant 
PrP substrates (i.e., RT-QuIC methodology) to: (1) investigate antemortem CWD 
detection, and (2) model PrP-based species barriers and trans-species 
adaptation-topics we previously explored using sPMCA and in vivo bioassays. At 
this symposium, we report sensitive and specific detection CWD prions in saliva, 
urine, blood (Mathiason lab), and rectal and pharyngeal lymph node samples 
(Haley NJ, et al.) from pre-symptomatic and symptomatic experimentally and 
naturally exposed deer. Other ongoing studies are employing RT-QuIC methodology 
to model amplification barriers among CWD, FSE, BSE, and CJD prions using 
cervine, feline, bovine, human, and promiscuous rPrP substrates and the above 
species prion seeds, cellular co-factors, and transgenic mice. Finally, in 
collaboration with the Wisniewski laboratory, we are conducting of experimental 
CWD vaccination studies in deer employing oral administration of an attenuated 
Salmonella vector expressing cervid PrP epitopes. 
===== 
AD.06: Detecting prions in the brain and blood of TSE-infected deer and 
hamsters 
Alan Elder,1 Davin Henderson,1 Anca Selariu,1 Amy Nalls,1 Byron Caughey,2 
Richard Bessen,1 Jason Bartz3 and Candace Mathiason1 
1Colorado State University; Fort Collins, CO USA; 2NIH Rocky Mountain 
Laboratories; Hamilton, MT USA; 3Creighton University; Omaha, NE USA 
While large quantities of protease resistant prion protein (PrPres) can be 
demonstrated by western blot or IHC in lymphoid biopsies or post-mortem brain 
tissues harvested from prion-infected animals, these conventional assays are 
less reliable as means to detect the small quantities of prions thought to be 
present in bodily fluids or associated with early and asymptomatic phases of TSE 
disease. The Real Time-Quaking Induced Conversion (RT-QuIC) assay is capable of 
detecting prions at concentrations below the level of sensitivity of 
conventional assays and provides a real-time fluorescent readout negating the 
use of proteases. We have made modifications to the RT-QuIC assay to utilize it 
for the detection of PrPres in brain and blood harvested from various species 
infected with prions. In this study, we analyzed CWD-infected deer and 
CWD/TME-infected hamster whole blood to determine the effect of: 
(1) various anticoagulants, 
(2) freezing and 
(3) NaPTA precipitation. 
Brain tissue and blood collected from naive deer and hamsters served as 
negative controls. 
We were able to demonstrate amplifiable prions in 
(1) brain and blood samples harvested from CWD/TME-infected animals, 
(2) heparinized blood, 
(3) frozen vs. fresh blood and 
(4) NaPTA treated samples. 
The RT-QuIC assay is able to detect PrPres in various species of animals 
and shows promise as an antemortem diagnostic tool for blood-borne TSEs. 
===== 
 Sunday, July 21, 2013 
*** As Chronic Wasting Disease CWD rises in deer herd, what about risk for 
humans? 
Thursday, October 10, 2013 
CJD REPORT 1994 increased risk for consumption of veal and venison and lamb 
*** The potential impact of prion diseases on human health was greatly 
magnified by the recognition that interspecies transfer of BSE to humans by beef 
ingestion resulted in vCJD. While changes in animal feed constituents and 
slaughter practices appear to have curtailed vCJD, there is concern that CWD of 
free-ranging deer and elk in the U.S. might also cross the species barrier. 
Thus, consuming venison could be a source of human prion disease. Whether BSE 
and CWD represent interspecies scrapie transfer or are newly arisen prion 
diseases is unknown. Therefore, the possibility of transmission of prion disease 
through other food animals cannot be ruled out. There is evidence that vCJD can 
be transmitted through blood transfusion. There is likely a pool of unknown size 
of asymptomatic individuals infected with vCJD, and there may be asymptomatic 
individuals infected with the CWD equivalent. These circumstances represent a 
potential threat to blood, blood products, and plasma supplies. 
Sunday, August 11, 2013
Creutzfeldt-Jakob Disease CJD cases rising North America updated report 
August 2013
Creutzfeldt-Jakob Disease CJD cases rising North America with Canada seeing 
an extreme increase of 48% between 2008 and 2010
Sunday, October 13, 2013 
CJD TSE Prion Disease Cases in Texas by Year, 2003-2012
TSS


